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Search for 'valine AND leucine' in 'all pathways' in 'Homo sapiens' returned 68 results

SMP0000731

Pw000708 View Pathway
Drug Action

Josamycin Action Pathway

  • Matched Compounds: L-Valine … L-Leucine
  • Matched Compound Synonyms: (s)-valineValine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine
  • SMP0000711

    Pw000688 View Pathway
    Drug Action

    Tobramycin Action Pathway

  • Matched Compounds: L-Valine … L-Leucine
  • Matched Compound Synonyms: (s)-valineValine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine
  • SMP0000713

    Pw000690 View Pathway
    Drug Action

    Arbekacin Action Pathway

  • Matched Compounds: L-Valine … L-Leucine
  • Matched Compound Synonyms: (s)-valineValine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine
  • SMP0000726

    Pw000703 View Pathway
    Drug Action

    Rolitetracycline Action Pathway

  • Matched Compounds: L-Valine … L-Leucine
  • Matched Compound Synonyms: (s)-valineValine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine
  • SMP0000200

    Pw000069 View Pathway
    Disease

    Methylmalonic Aciduria

  • Matched Compounds: L-Leucine … L-Valine
  • Matched Compound Synonyms: (2s)-alpha-leucine … (s)-(+)-leucine … (s)-leucineLeucine … (2s)-a-leucine
  • SMP0000523

    Pw000499 View Pathway
    Disease

    Isobutyryl-CoA Dehydrogenase Deficiency

  • Matched Description: error of metabolism (IEM) of valine metabolism. It is an autosomal recessive disorder that is caused … the metabolism of branched-chain amino acids, specifically valine. This enzyme is responsible for … the third step in the breakdown of valine and converts isobutyryl-CoA into methylacrylyl-CoA. Defects … in the IBD enzyme function lead to elevated levels of valine in blood and other biofluids … energy. Treatment may include the use of L-carnitine supplements, frequent meals, and a low-valine diet.
  • Matched Compounds: L-Leucine … L-Valine
  • Matched Compound Synonyms: (2s)-alpha-leucine … (s)-(+)-leucine … (s)-leucineLeucine … (2s)-a-leucine
  • SMP0000199

    Pw000064 View Pathway
    Disease

    Maple Syrup Urine Disease

  • Matched Description: for a protein which is vital in the breakdown of amino acids, specifically the amino acids leucine … , isoleucine and valine. This disorder is characterized by a large accumulation of these amino acids
  • Matched Compounds: L-Leucine … L-Valine
  • Matched Compound Synonyms: (2s)-alpha-leucine … (s)-(+)-leucine … (s)-leucineLeucine … (2s)-a-leucine
  • SMP0125662

    Pw127227 View Pathway
    Disease

    3-Methylcrotonyl-CoA Carboxylase Deficiency Type I

  • Matched Description: constitute the breakdown of leucine. Mutations in the aforementioned genes leads to a reduction in the … breakdown leucine properly. Consequently, this leads to the build up of toxic byproducts which are not … processed as the breakdown of leucine is left incomplete. If these toxic byproducts manifest themselves
  • Matched Compounds: L-Valine … L-Leucine
  • Matched Compound Synonyms: (s)-valineValine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine
  • SMP0125669

    Pw127234 View Pathway
    Disease

    Methylmalonate Semialdehyde Dehydrogenase Deficiency

  • Matched Compounds: L-Valine … L-Leucine
  • Matched Compound Synonyms: (s)-valineValine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine
  • SMP0125657

    Pw127222 View Pathway
    Disease

    beta-Ketothiolase Deficiency

  • Matched Compounds: L-Valine … L-Leucine
  • Matched Compound Synonyms: (s)-valineValine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine